Document Details
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Document Type |
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Article In Journal |
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Document Title |
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Dandy Walker Malformation and Hypertrophic Cardiomyopathy: Unusual Fatal Association. حلة نادرة و مميتة لمتلازمة الداندي واكر و اعتلال عضلة القلب المتضخمة |
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Document Language |
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English |
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Abstract |
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Dandy Walker malformation (DWM) is a rare congenital brain anomaly characterized by cystic dilation of the fourth ventricle and hypoplasia of the cerebellar vermis. Other extracranial anomalies can be associated, including cardiac defects. We report a rare patient with DWM associated with progressive heart failure secondary to hypertrophic cardiomyopathy. He was diagnosed at 2 months of age and died 5 months later. This syndromic association has not been previously noted in the literature. We conclude that hypertrophic cardiomyopathy can be associated with DWM with poor prognosis. Careful cardiac evaluation is needed in all infants with DWM for early recognition of such potentially serious associated cardiac malformations. |
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ISSN |
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0379-5284 |
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Journal Name |
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Neurosciences Journal |
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Volume |
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4 |
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Issue Number |
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14 |
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Publishing Year |
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2009 AH
2009 AD |
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Article Type |
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Article |
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Added Date |
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Wednesday, March 10, 2010 |
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Researchers
| محمد جان | jan, Mohammed | Researcher | Doctorate | |
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